Successful kidney retransplantation after combined liver/kidney transplantation in primary hyperoxaluria type I.
نویسندگان
چکیده
Key words: combined liver/kidney transplantation; reference range of 20–40 mmol/l. Prior to analysis, an nephrocalcinosis; primary hyperoxaluria ultrafiltration of plasma to remove proteins and others molecules was performed. Urine ion chromatography was used for measuring urine oxalate concentration with a reference range of
منابع مشابه
Oxalosis with nephrocalcinosis.
Primary hyperoxaluria type I is a rare autosomal show reflux. Cystoscopy with retrograde urogram showed no evidence of obstruction. A diagnosis of recessive metabolic disorder characterized by absence of liver specific peroxisomal alanine glyoxylate aminoend-stage renal disease (ESRD) of unknown aetiology was made. Live related donor kidney transplant was transferase (AGT ) leading to elevated ...
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Primary hyperoxaluria type 1 is an autosomal recessive hereditary glyoxylate metabolism disorder characterized by excessive production of oxalate, caused by the deficiency of liver specific peroxisomal enzyme: alanineglyoxylate aminotransferase. For patients with end-stage renal disease, combined liver and kidney transplantation was needed. This report describes one patient, with a diagnosis of...
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ورودعنوان ژورنال:
- Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association
دوره 13 6 شماره
صفحات -
تاریخ انتشار 1998